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Maksud "gargoylism" dalam kamus Corsica

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SEBUTAN GARGOYLISM DALAM CORSICA

gargoylism  [ˈɡɑːɡɔɪlɪzəm] play
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KATEGORI TATABAHASA GARGOYLISM

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APAKAH MAKSUD GARGOYLISM dalam CORSICA?

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Sindrom Hurler

Hurler syndrome

Sindrom Hurler, juga dikenali sebagai mucopolysaccharidosis type I, penyakit Hurler, juga gargoylism, adalah gangguan genetik yang mengakibatkan pembentukan glycosaminoglycans disebabkan oleh kekurangan alpha-L iduronidase, enzim yang bertanggungjawab terhadap kemerosotan mucopolysaccharides di lisosomes. Tanpa enzim ini, pembentukan heparan sulfat dan dermatan sulfat berlaku di dalam badan. Gejala timbul semasa kanak-kanak dan kematian awal boleh berlaku akibat kerosakan organ. MPS I dibahagikan kepada tiga subtipe berdasarkan keparahan gejala. Kesemua tiga jenis hasil daripada ketiadaan, atau tahap yang tidak mencukupi, enzim α-L-iduronidase. Sindrom MPS I H atau Hurler adalah yang paling parah dari subtipe MPS I. Dua lagi jenis adalah sindrom MPS I S atau Scheie dan sindrom MPS I H-S atau Hurler-Scheie. Sindrom Hurler sering diklasifikasikan sebagai penyakit penyimpanan lysosomal, dan secara klinikalnya berkaitan dengan Sindrom Hunter. Sindrom Hunter adalah berkaitan dengan X manakala sindrom Hurler adalah autosomal resesif. Ia dinamakan untuk Gertrud Hurler, pakar kanak-kanak Jerman. Hurler syndrome, also known as mucopolysaccharidosis type I, Hurler's disease, also gargoylism, is a genetic disorder that results in the buildup of glycosaminoglycans due to a deficiency of alpha-L iduronidase, an enzyme responsible for the degradation of mucopolysaccharides in lysosomes.:544 Without this enzyme, a buildup of heparan sulfate and dermatan sulfate occurs in the body. Symptoms appear during childhood and early death can occur due to organ damage. MPS I is divided into three subtypes based on severity of symptoms. All three types result from an absence of, or insufficient levels of, the enzyme α-L-iduronidase. MPS I H or Hurler syndrome is the most severe of the MPS I subtypes. The other two types are MPS I S or Scheie syndrome and MPS I H-S or Hurler-Scheie syndrome. Hurler syndrome is often classified as a lysosomal storage disease, and is clinically related to Hunter Syndrome. Hunter syndrome is X-linked while Hurler syndrome is autosomal recessive. It is named for Gertrud Hurler, a German pediatrician.

Definisi gargoylism dalam kamus Corsica

Takrif gargoylism dalam kamus adalah keadaan perubatan yang dicirikan oleh kecacatan fizikal dan kekurangan mental, kini lebih dikenali sebagai sindrom Hurler.

The definition of gargoylism in the dictionary is a medical condition characterized by physical deformity and mental deficiency, now more commonly known as Hurler's syndrome.

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Klik untuk melihat terjemahan automatik definisi dalam Melayu.

CORSICA PERKATAAN YANG BERIMA DENGAN GARGOYLISM


alcoholism
ˈælkəhɒˌlɪzəm
brachydactylism
ˌbrækɪˈdæktɪlɪzəm
capitalism
ˈkæpɪtəˌlɪzəm
didactylism
daɪˈdæktɪlɪzəm
gentilism
ˈdʒentɪlɪzəm
heterostylism
ˌhɛtərəʊˈstaɪlɪzəm
journalism
ˈdʒɜːnəˌlɪzəm
metabolism
mɪˈtæbəˌlɪzəm
nationalism
ˈnæʃənəˌlɪzəm
pentadactylism
ˌpentəˈdæktɪlɪzəm
polydactylism
ˌpɒlɪˈdæktɪlɪzəm
professionalism
prəˈfɛʃənəˌlɪzəm
realism
ˈrɪəˌlɪzəm
socialism
ˈsəʊʃəˌlɪzəm
surrealism
səˈrɪəˌlɪzəm
symbolism
ˈsɪmbəˌlɪzəm
syndactylism
sɪnˈdæktɪlɪzəm
troilism
ˈtrɔɪlɪzəm
vandalism
ˈvændəˌlɪzəm
zygodactylism
ˌzaɪɡəʊˈdæktɪlɪzəm

CORSICA PERKATAAN YANG BERMULA SEPERTI GARGOYLISM

garganey
Gargantua
gargantuan
gargarise
gargarism
garget
gargety
gargle
gargler
gargoyle
gargoyled
gari
garial
garibaldi
garigue
garish
garishly
garishness
garland
garlandage

CORSICA PERKATAAN YANG BERAKHIR SEPERTI GARGOYLISM

brutalism
citizen journalism
colonialism
embolism
formalism
idealism
imperialism
individualism
liberalism
literalism
materialism
minimalism
multiculturalism
odylism
Orientalism
parallelism
photojournalism
pluralism
pointillism
salicylism

Sinonim dan antonim gargoylism dalam kamus sinonim Corsica

SINONIM

Terjemahan «gargoylism» ke dalam 25 bahasa

PENTERJEMAH
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TERJEMAHAN GARGOYLISM

Cari terjemahan gargoylism kepada 25 bahasa dengan penterjemah Corsica pelbagai bahasa kami.
Terjemahan gargoylism dari Corsica ke bahasa lain yang dibentangkan dalam bahagian ini telah diperolehi menerusi terjemahan statistik automatik; di mana unit terjemahan penting adalah perkataan «gargoylism» dalam Corsica.

Penterjemah Corsica - Cina

gargoylism
1,325 juta pentutur

Penterjemah Corsica - Czech

gargolismo
570 juta pentutur

Corsica

gargoylism
510 juta pentutur

Penterjemah Corsica - Hindi

gargoylism
380 juta pentutur
ar

Penterjemah Corsica - Amhara

غرقلية
280 juta pentutur

Penterjemah Corsica - Rusia

gargoylism
278 juta pentutur

Penterjemah Corsica - Punjabi

gargoylism
270 juta pentutur

Penterjemah Corsica - Basque

gargoylism
260 juta pentutur

Penterjemah Corsica - Frisia

gargoylisme
220 juta pentutur

Penterjemah Corsica - Melayu

Gargoylism
190 juta pentutur

Penterjemah Corsica - Chichewa

Gargoylismus
180 juta pentutur

Penterjemah Corsica - Jepun

gargoylism
130 juta pentutur

Penterjemah Corsica - Kreol Haiti

gargoylism
85 juta pentutur

Penterjemah Corsica - Jerman

Gargoylism
85 juta pentutur
vi

Penterjemah Corsica - Vietnam

gargoylism
80 juta pentutur

Penterjemah Corsica - Tagalog

gargoylism
75 juta pentutur

Penterjemah Corsica - Marathi

नागमोडीपणा
75 juta pentutur

Penterjemah Corsica - Turki

gargoilızm
70 juta pentutur

Penterjemah Corsica - Itali

gargoylism
65 juta pentutur

Penterjemah Corsica - Poland

gargoylism
50 juta pentutur

Penterjemah Corsica - Ukraine

gargoylism
40 juta pentutur

Penterjemah Corsica - Romania

gargoylism
30 juta pentutur
el

Penterjemah Corsica - Cina

gargoylism
15 juta pentutur
af

Penterjemah Corsica - Afrikaans

gargoylism
14 juta pentutur
sv

Penterjemah Corsica - Swahili

gargoylism
10 juta pentutur
no

Penterjemah Corsica - Parsi

gargoylism
5 juta pentutur

Aliran kegunaan gargoylism

ALIRAN

KECENDERUNGAN PENGGUNAAN TERMA «GARGOYLISM»

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Peta yang ditunjukkan di atas memberikan kekerapan penggunaan terma «gargoylism» dalam negara berbeza.
Kecenderungan carian utama dan penggunaan umum gargoylism
Senarai carian utama yang dibuat oleh pengguna untuk mengakses kamus Corsica dalam talian kami dan ungkapan yang paling banyak digunakan dengan perkataan «gargoylism».

KECENDERUNGAN PENGGUNAAN TERMA «GARGOYLISM» DARI MASA KE MASA

Grafik menyatakan evolusi tahunan kekerapan penggunaan perkataan «gargoylism» selama 500 tahun yang lalu. Pelaksanaannya adlah berdasarkan kepada menganalisa kekerapan istilah «gargoylism» muncul dalam sumber bercetak digital dalam Corsica antara tahun 1500 dan hari ini.

Contoh penggunaan dalam kesusasteraan Corsica, petikan dan berita mengenai gargoylism

CONTOH

CORSICA BUKU YANG BERKAIT DENGAN «GARGOYLISM»

Ketahui penggunaan gargoylism dalam pilihan bibliografi berikut. Buku yang berkait dengan gargoylism dan ekstrak ringkas dari yang sama untuk menyediakan konteks penggunaannya dalam kesusasteraan Corsica.
1
Chemistry and Biology of Mucopolysaccharides
Barker and Stacey (1956) made use of this fact in studying the polysaccharide content of the liver from a gargoylism case. The water-extracted polysaccharides were separated by Cetavlon into neutral and acidic fractions. The neutral fraction  ...
CIBA Foundation Symposium, 2009
2
Left Behind: A Study of Mental Handicap
Gargoylism One of the most easily recognised conditions due to inborn metabolic errors is gargoylism, so called because of the distinctive facial appearance, which is said to resemble that of a gargoyle. This condition is inherited in both ...
W. Alan Heaton-Ward, 2014
3
MacSween's Pathology of the Liver
336 Lindsay S, Reilly WA, Gotham TJ, Skahen R. Gargoylism. II. Study of pathologic lesions and clinical review of twelve cases. Am J Dis Child. 1948;76: 239-306. 337 Wolfe HJ, Blennerhauser J B, Young GF, Cohen RB. Hurler's syndrome.
Alastair D. Burt, Bernard C. Portmann, Linda D. Ferrell, 2011
4
Encyclopedia of Special Education, 3 Volume Set
Cecil R. Reynolds, Elaine Fletcher-Janzen. 948 GARGOYLISM 950 GEARHEART, BILL R. (1918–2001) 952 GENERALIZATION 954 GENETIC COUNSELING. GARGOYLISM. See HURLER SYNDROME. GARRETT,. EMMA. ( 1846–1893).
Cecil R. Reynolds, Elaine Fletcher-Janzen, 2007
5
General Principles of Orthopedics and Trauma
Gargoylism-Hunter's. Syndrome. The characteristic histological feature is the presence of clear cells or fibroblasts, distended by some glycoprotein material throughout the connective tissue, meninges, and cornea, which are sometimes called ...
K Mohan Iyer, 2012
6
Dictionary of Medicine
galistone. gargoylism. a serious condition can develop if a gallstone blocks the bile duct. Sudden pain going from (he right side of the stomach towards the back indicates that a gallstone is passing through the bile duct galvanism noun ...
P.H. Collin, 2014
7
The Molecular and Genetic Basis of Neurologic and ...
1919:24:220-234. 9. Ellis RWB, Sheldon W, Capon NB. Gargoylism (chondroos- teo-dystrophy, corneal opacities, hepato-splenomegaly, and mental deficiency). Q J Med. 1936;5:1 19-139. 10. Brante G. Gargoylism: a mucopolysaccharidosis.
Roger N. Rosenberg, 2008
8
Developmental Neuropsychiatry: Assessment, Diagnosis, and ...
Gargoylism: A mucopolysacchari- dosis. Scandinavian Journal of Clinical Laboratory Investigation, 4:43-46. Cleary, M.A., and Wraith, J.E. (1993). Management of mucopolysaccharidosis Type III. Archives of Disease in Childhood, 69:403-406.
James C. Harris, 1998
9
Biochemical Basis of Inherited Human Disease
Miss Thelma Atkinson performed many of the analytic procedures. REFERENCES 1. Hunter, C. A rare disease in two brothers. Proc. Roy. Soc. Med. , 10: 104. 1917. 2. Brante, C. Gargoylism: a mucopolysaccharidosis. Scandinav. ]. Clin. & Lab.
‎1973
10
Heart disease in infancy and childhood
Ashby, W. R.; Stewart, R. M.; and Watkin, J. H.: Chondro-osteo-dystrophy of the Hurler type (gargoylism): a pathological study. Brain, 60:149, 1937. Berenson, G. S., and Geer, J. C: Heart disease in the Hurler and Marfan syndromes. Arch Intern ...
John D. Keith, Richard Desmond Rowe, Peter Vlad, 1967

BARANGAN BERITA YANG TERMASUK TERMA «GARGOYLISM»

Ketahui apa yang diterbitkan oleh akhbar nasional dan antarabangsa dan cara istilah gargoylism digunakan dalam konteks perkara berita berikut.
1
No-knife surgery's become as routine as getting a haircut
Reddy says the gargoylism problem arises because the industry is not regulated. "The problem with this selfie generation and collective ... «Times LIVE, Jun 15»
2
Dr. Andre Morato: We're not playing God; we only want a better …
We also have a 14-year-old child with gargoylism (a genetic disorder named after Gargoyle because the sufferer looks grotesque, too). «Philippine Star, Nov 13»
3
Review by Leo Uzych, JD, MPH
Mary Craig, for example, is the contributor of an essay (Chapter 5) about her son, Paul, who had gargoylism, and died eventually at age 10. «Metapsychology, Ogo 12»
4
The suffering son who gave me so much
That horrible word “gargoylism” was working its poison and I recoiled before a future in which I was some kind of pariah, shunned by everyone. «Catholic Herald Online, Jun 11»
5
Monumental in proportion alone
"It's a kind of form of gargoylism, in a certain way, that had grown very monumental and doo-dadish and just plonked on the pavement.". «The Age, Mei 11»
6
Book Of A Lifetime: Blessings, By Mary Craig
The book covers the short life of Craig's second son, Paul, born in 1956 with Hohler's Syndrome, crudely called gargoylism, which left him ... «The Independent, Apr 11»
7
Consultant recalls clashes with hierarchy
... possibility of arranging an antenatal test in the UK for a woman whose previous child had been born with a congenital condition, gargoylism. «Irish Health, Jan 11»
8
Troublesome gene names get the boot
"We don't use terms like gargoylism or mongoloidism any more, and yet we still have these gene names like lunatic that are quite fanciful," he ... «Nature.com, Nov 06»

RUJUKAN
« EDUCALINGO. Gargoylism [dalam talian]. <https://educalingo.com/ms/dic-en/gargoylism> Tersedia. Mei 2024 ».
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